Write-up by Juliet Cohen
Cystic lymphangioma is a rare tumour, often situated in the cervical or axillary region and exceptionally intraabdominal. It is essentially a malformation of 1 of the abdominal lymph vessels where a portion is dilated and form a lymph fluid-filled cyst. Abdominal lymphangiomas are far more typical in boys and normally happen in childhood. It arises due to a congenital defect in the connection of the main lymphatic channels with the central collecting program. It presents clinically either in the form of a pseudo-appendix or pseudo-ascites syndrome or in the form of an abdominal tumour with or without having compression of adjacent structures. The clinical symptoms are variable. Chronic symptoms consist of chronic abdominal pain and progressive abdominal distension.
Cysts are thought to originate from lymphatic spaces linked with the immature retroperitoneal lymph sac, producing them similar to cystic hygromas, which originate in the neck in association with the jugular lymph sac. Yet another proposed etiology is lymphatic interference. The tumor is a hamartoma or vascular developmental anomaly arising from lymphatic vessels, manifesting as a raised, tender, bushy, bubbly, pinkish-white lesion esthetic considerations may justify attempted removal of lymphangiomas. Mesenteric and omental cysts can be straightforward or dual, unilocular or multilocular, and they might carry hemorrhagic, serous, chylous, or contaminated fluid. The fluid is serous in ileal and colonic cysts and is chylous in jejunal cysts.
Acute symptoms usually contain intense abdominal discomfort and distension, vomiting, fever and peritonitis. Though an abdominal lymphangioma is considered harmless, it could get locally intrusive. For that reason any involved organ should too be resected. Incomplete resection may head to recurrence. If the patient was treated with marsupialization, closer follow-up for possible recurrence need to be instituted. Otherwise, no long-term follow-up for postoperative problems is necessary. Intraabdominal lymphangiomas are harmless lesions but thinking about their local intrusive holding comprehensive resection of the cyst along with involved organ and clinical and radiological come upward for recurrence is required.
The prognosis of lymphangiomas depends on the position and extent of the lesion and the presence of new linked abnormalities. Genetic syndromes that are linked with cystic hygroma include Turner syndrome and some trisomies e. g. trisomy 13, 18 and 21. Total resection is the treatment of selection and has an excellent prognosis. Despite the fact that an abdominal lymphangioma is considered benign, it might turn out to be locally invasive. Even though an abdominal lymphangioma is regarded as benign, it could turn into locally invasive. As a result any involved organ should also be resected. Incomplete resection might lead to recurrence. Treatment is well defined and consists of surgical resection of the isolated lymphangioma or associated with the adjacent intestine, depending on the internet site of the tumour. It has a very good prognosis.
About the Author
Alicia Stock writes articles for well being physician. She also writes articles for haircut styles and beauty guidelines.
Our journey with our daughter, as she is diagnosed with a cystic hygroma and the eventual surgery.
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